Pediatria pre prax 3/2025
Anesthesia in children with osteogenesis imperfecta
Osteogenesis imperfecta is a heterogeneous group of inherited connective tissue disorders characterized by increased bone fragility and a high incidence of fractures. In its more severe forms, respiratory and cardiovascular complications significantly increase the perioperative risk. This article reviews the specific anesthetic considerations in children with osteogenesis imperfecta and identifies key factors influencing the safe administration of anesthesia. It focuses on comprehensive preoperative assessment, careful patient handling during positioning and airway management, challenges in establishing vascular access, appropriate selection of anesthetic techniques, fracture risk evaluation, and individualized anesthetic planning. Drawing on the current literature and clinical experience, this review provides recommendations to optimize perioperative care in this vulnerable pediatric population.
Keywords: osteogenesis imperfecta, pediatric anesthesia, airway management, fractures, perioperative care
